Alport syndrome with pelvic leiomyomatosis: The role of hormonal suppression

نویسندگان

چکیده

Introduction: Alport syndrome with diffuse pelvic leiomyomatosis is a complex combination for which the course of treatment not well described. This case describes outcomes trial gonadotropin-releasing hormone analogues as an alternative to extensive surgery. Case Report: A 47-year-old female patient, known associated leiomyomatosis, was referred our gynecological service because mass. The patient complained obstipation and pain in right hypochondrium. Magnetic resonance imaging showed multi-lobulated from vulvar perineal area. As removal mass would imply very surgery, conservative options were searched for, analogy medical uterine leiomyomas. few trials used but follow-up data these articles are lacking. For this who close menopausal age, therapy followed by adnexectomy total hormonal suppression. patient’s stabilization decrease complaints. Conclusion: demonstrates that suppression can be successful surgery combining leiomyomatosis.

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ژورنال

عنوان ژورنال: Journal of Case Reports and Images in Obstetrics and Gynecology

سال: 2022

ISSN: ['2582-0249']

DOI: https://doi.org/10.5348/100125z08cv2022cr